Primary Pulmonary Hypertension and Moyamoya Disease: Case Presentation and Review of Literature
| Author | Fatemeh Vaziri | en |
| Author | Shahla Roodpeyma | en |
| Author | Narges Ashrafinia | en |
| Issued Date | 2013-08-10 | en |
| Abstract | Introduction: Primary pulmonary hypertension (PPH) is an uncommon disease in children. This pulmonary vascular disease may be idiopathic, familial or a kind of hereditary systemic vasculopathy. Multisystemic vascular diseases in children are rare and may be under-recognized. A few reports have described the involvement of cerebral vessels such as moyamoya disease (MD) in patients with PPH. MD is a unique cerebrovasculopathy, characterized by occlusion of the internal carotid arteries. Case Presentation: We reported a 2-year-old boy with PPH, who presented unusual and intractable seizure which suggested the diagnosis of MD. We also reviewed a few previous reports about the association of PPH with moyamoya disease. Discussion: Moyamoya disease is a kind of cerebral vasculopathy and should be considered as a differential diagnosis for patients with unusual seizure attacks who are suffering from primary pulmonary hypertension. | en |
| DOI | https://doi.org/10.17795/compreped-11143 | en |
| Keyword | Moyamoya Disease | en |
| Keyword | Pulmonary Hypertension | en |
| Keyword | Vascular Diseases | en |
| Publisher | Brieflands | en |
| Title | Primary Pulmonary Hypertension and Moyamoya Disease: Case Presentation and Review of Literature | en |
| Type | Case Report | en |
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