A case report of Merckle Cell carcinoma in medial wall of orbit

Abstract

Merckle cell carcinoma (MCC) is a relatively rare tumor, originating from Neuroendocrine cells, with aggressive behavior and common recurrence.It is more common in males and in head and neck region.Pathologists diagnose it by immunohistochemical staining (IHC). Its definite treatment is not still determined, however radical resection as the main cure and radiotherapy as the supporting treatment are suggested. Based on many reports the most common site of MCC in head and neck region is cheeck and eyelid. The site of MCC in this report is the medial wall of orbit, about which no report was found in medical literature. The interesting point in this case presentation is that one of the differential diagnoses of mass lesions in the medial wall of orbit is MCC and the colleagues should pay attention to this rare disease in such instances. Presently the reported case is under control with surgery and radiotherapy and chemotherapy.