Pachydermoperiostosis: A case report
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Date
2002-09-30
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Brieflands
Abstract
Primary Pachydermoperiostosis is a rare hereditary disease characterized by folded coarse
skin, hyperostosis, clubbing and abnormality in other organ such as gastrointestinal tract.
This syndrome is autosomal dominant with variable expressivity, but a family with autosomal
recessive had also been reported. Disease occurs predominantly in men. Secondary form is
usually a provoked by sever pulmonary disease. Treatment is symptomatic. This is a case report
of such patient from Baloochestan, Iran.