Burden of Congenital Factor XIII Deficiency in Iran

Author	Akbar Dorgalaleh	en
Issued Date	2017-09-30	en
Abstract	Congenital factor XIII (FXIII) deficiency is a rare coagulopathy with the highest incidence in Iran. Iranian patients with FXIII deficiency (FXIIID) presented high rate of bleeding episodes, some of them are major cause of disability and mortality among these patients. Hemarthrosis and intracranial hemorrhage (ICH) can affect activity and social productivity of patients. ICH, recurrent miscarriage and umbilical cord bleeding are the major cause of mortality. Hematoma, and prolonged menstrual bleeding as well as post-surgical bleeding are other significant bleeding in Iranian patients with FXIIID. Present of severe life threatening bleeding episodes and other notable bleedings, can significantly reduce working activities and social productivities of patients. Although Iranian patients with FXIIID, experienced significant diseases related complications, early diagnosis accompany by appropriate therapeutic regimes can prevent most of these problems.	en
DOI	https://doi.org/10.22037/jcma.v2i3.16263	en
Keyword	Congenital Factor XIII Deficiency	en
Keyword	coagulopathy	en
Keyword		en
Publisher	Brieflands	en
Title	Burden of Congenital Factor XIII Deficiency in Iran	en
Type	Review	en

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