Improvement of Dilated Cardiomyopathy with Methylprednisolone in a Patient with Multiple Fibrosclerosis

AuthorIbrahim Altunen
AuthorGoksel Guzen
AuthorFatih Akinen
AuthorNuri Koseen
AuthorIlknur Altunen
AuthorZeki Yuksel Gunaydinen
AuthorCem Sahinen
Issued Date2014-12-31en
AbstractMultifocal fibrosclerosis is a rare syndrome of unknown cause that is characterized by fibrosis involving multiple organ systems. Definitive diagnosis can only be made based on biopsy findings. In this case, the biopsy specimen of the patient demonstrates pulmonary hyalinated granuloma or sclerosing mediastinitis. There are few reports of multiple fibrosclerosis with heart failure. Here, we reported a case of retroperitoneal fibrosis with massive mediastinal involvement extending to pleura and pericardium causing pleuro- pericardial effusion with dilated cardiomyopathy. Systolic dysfunction was improved and pericardial effusion disappeared with methylprednisolone treatment.en
DOIhttps://doi.org/en
KeywordMultifocal Fibrosclerosisen
KeywordDilated Cardiomyopathyen
KeywordMyocarditisen
KeywordPulmonary Hyalinated Granulomaen
KeywordSclerosing Mediastinitisen
PublisherBrieflandsen
TitleImprovement of Dilated Cardiomyopathy with Methylprednisolone in a Patient with Multiple Fibrosclerosisen
TypeCase Reporten

Files

Original bundle

Now showing 1 - 1 of 1
Loading...
Thumbnail Image
Name:
icrj-08-178.pdf
Size:
840.8 KB
Format:
Adobe Portable Document Format
Description:
Article/s PDF